Arrhythmogenic Right Ventricular Cardiomyopathies

Implantable cardioverter defibrillator in arrhythmogenic right ventricular cardiomyopathies.

In the present issue of Circulation, Wichter et al 1 report the largest single-center experience demonstrating the benefit of implantable cardiac defibrillators (ICDs) in the treatment of patients with arrhythmogenic right ventricular cardiomyopathy (ARVC). The patients seem well defined, and they meet the task force criteria. In addition, 50 of 60 patients have had the diagnosis confirmed by e...

Arrhythmogenic right ventricular cardiomyopathies: clinical forms and main differential diagnoses.

Arrhythmogenic right ventricular dysplasia.

The clinical course in 15 patients with features consistent with arrhythmogenic right ventricular dysplasia is described. At referral seven patients had abnormal physical findings, nine had abnormal electrocardiograms with non-specific right-sided abnormalities, and seven patients had increased heart size or prominent right ventricles on chest x ray. During long term follow up (mean 8 8 years, ...

Arrhythmogenic Right Ventricular Cardiomyopathy

Arrythmogenic right ventricular (RV) cardiomyopathy (ARVC) is a cardiomyopathy characterized pathologically by fibrofatty replacement primarily of the RV and clinically by life-threatening ventricular arrhythmias in apparently healthy young people. The prevalence of the disease has been estimated at 1 in 5,000 individuals, although this estimate will likely increase as awareness of the conditio...

Arrhythmogenic right ventricular cardiomyopathy.

Arrhythmogenic right ventricular cardiomyopathy (ARVC) has evolved from postmortem pathology at to a diagnosable clinical condition, and holds promise for definitive genetic diagnosis. Its prevalence is between 1/1,000 and 1/5,000, with 10% of deaths occurring before age 19 and 50% before age 35. When analyzed against age-specific norms, the electrocardiography (ECG) and signal-averaged ECG (SA...